Skin Manifestations of Neurocutaneous Syndromes, Among Sudanese Children Attending Outpatient Clinic of Soba University Hospital

Abstract

Background: The neuroccutaneous syndromes are a group of diseases where characteristic skin lesions are seen in association with abnormalities of the central nervous system, and by consequence are at risk of developing epilepsy and other co morbidities. Aim and Objectives: The objective of this study was to list skin manifestations among Sudanese children with neuroccutaneous syndrome, attending outpatient clinic of Soba University Hospital, 2015. Material and Methods: This is a cross sectional hospital based study, fifty children with neuroccutaneous syndrome, were included in the study, and aged between 6 months to 15 years, from April 2014-April 2015, the data was collected by designed check sheet, and detailed skin examination was done and reviewed by dermatologist. Results: The mean age of the whole study group was 4.45 ±1.96 years. The majority of study group were in the age group 1-5 years constituting 36% of total population of the study. Thirty seven patients (74%) were males and 13 patients were females 26%, male, 24 % of patients presented complained of skin lesions from total patients, the most common skin lesion is ash leaves. Conclusion: Skin manifestations, hypopigmented skin patches (ash leaves) was the commonest lesion, and help in early diagnosis.

Keywords

• Neuroccutaneous syndromes
• Sudanese
• skin lesion
• Tuberous sclerosis
• subependymal tuber