Non Specific Interstitial Pneumonia: A Case Report

Abstract

Idiopathic Non-Specific Interstitial Pneumonia (NSIP) is a rare entity in children and classified into cellular NSIP (c-NSIP) or fibrotic NSIP patterns. It comes under major idiopathic interstitial pneumonia. Both conditions are characterised by Ground Glass Opacities (GGO), irregular linear opacities and consolidations in a bilateral, symmetrical or sub pleural distribution. It’s a disease with diagnostic difficulty so a multidisciplinary diagnosis was approached for the diagnosis i.e., clinical, radiological and histopathological. The prognosis of this condition is variable; it is a reversible disease with risk of progression. Therefore, early diagnosis and disease stratification are important in this disease. Here we report the case of a three-year-old girl child who presented with atypical clinical and radiological features, but had been diagnosed to have c-NSIP.

Keywords

• ground glass opacity
• interstitial lung disease
• lung biopsy