Dermatopathia pigmentosa reticularis

Abstract

Dermatopathia pigmentosa reticularis (DPR) is a rare disorder with characteristic triad of generalized reticulate hyperpigmentation, noncicatricial alopecia, and onychodystrophy. A 12-year-old Indian boy presented with classical features of the triad along with adermatoglyphia, hyperhidrosis, punctate hyperkeratosis of palm, and sole along with keratosis pilaris. Histopathology suggested a diagnosis of DPR with a differential of Naegeli–Franceschetti–Jadassohn syndrome and dyskeratosis congenita.

Keywords

• Dermatopathia pigmentosa reticularis
• dyskeratosis congenita
• histopathology
• keratosis pilaris
• Naegeli–Franceschetti–Jadassohn syndrome