Related liver fragment transplantation for type 1 glycogenosis: the first Russian experience The paper describes two clinical examples of successful related liver fragment transplantation for type 1 glycogenosis in a one-year-old boy and a 6-year-old girl. The given first successful clinical experience suggests that liver fragments for type 1 glycogenoses can be transplanted from live related donors and offers promise for the radical treatment of patients with this pathology.

A. V. Filin; A. V. Semenkov; N. A. Koroteyeva; A. Ya. Keligova; A. V. Metelin; E. F. Kim; D. S. Dzhamanchin; N. E. Khartukova; Yu. R. Kamalov; E. Yu. Kryzhanovskaya; V. A. Khovrin; T. N. Galyan; B. S. Kaganov; E. N. Kutyreva; A. I. Zubovich

doi:10.23873/2074-0506-2011-0-2-3-24-28

Трансплантология (Москва) (Aug 2018)

Related liver fragment transplantation for type 1 glycogenosis: the first Russian experience The paper describes two clinical examples of successful related liver fragment transplantation for type 1 glycogenosis in a one-year-old boy and a 6-year-old girl. The given first successful clinical experience suggests that liver fragments for type 1 glycogenoses can be transplanted from live related donors and offers promise for the radical treatment of patients with this pathology.

A. V. Filin,
A. V. Semenkov,
N. A. Koroteyeva,
A. Ya. Keligova,
A. V. Metelin,
E. F. Kim,
D. S. Dzhamanchin,
N. E. Khartukova,
Yu. R. Kamalov,
E. Yu. Kryzhanovskaya,
V. A. Khovrin,
T. N. Galyan,
B. S. Kaganov,
E. N. Kutyreva,
A. I. Zubovich

Affiliations

A. V. Filin: Acad. B.V. Petrovsky Russian Surgery Research Center, Russian Academy of Medical Sciences; Research Institute of Nutrition, Russian Academy of Medical Sciences
A. V. Semenkov: Acad. B.V. Petrovsky Russian Surgery Research Center, Russian Academy of Medical Sciences; Research Institute of Nutrition, Russian Academy of Medical Sciences
N. A. Koroteyeva: Acad. B.V. Petrovsky Russian Surgery Research Center, Russian Academy of Medical Sciences; Research Institute of Nutrition, Russian Academy of Medical Sciences
A. Ya. Keligova: Acad. B.V. Petrovsky Russian Surgery Research Center, Russian Academy of Medical Sciences; Research Institute of Nutrition, Russian Academy of Medical Sciences
A. V. Metelin: Acad. B.V. Petrovsky Russian Surgery Research Center, Russian Academy of Medical Sciences; Research Institute of Nutrition, Russian Academy of Medical Sciences
E. F. Kim: Acad. B.V. Petrovsky Russian Surgery Research Center, Russian Academy of Medical Sciences; Research Institute of Nutrition, Russian Academy of Medical Sciences
D. S. Dzhamanchin: Acad. B.V. Petrovsky Russian Surgery Research Center, Russian Academy of Medical Sciences; Research Institute of Nutrition, Russian Academy of Medical Sciences
N. E. Khartukova: Acad. B.V. Petrovsky Russian Surgery Research Center, Russian Academy of Medical Sciences; Research Institute of Nutrition, Russian Academy of Medical Sciences
Yu. R. Kamalov: Acad. B.V. Petrovsky Russian Surgery Research Center, Russian Academy of Medical Sciences; Research Institute of Nutrition, Russian Academy of Medical Sciences
E. Yu. Kryzhanovskaya: Acad. B.V. Petrovsky Russian Surgery Research Center, Russian Academy of Medical Sciences; Research Institute of Nutrition, Russian Academy of Medical Sciences
V. A. Khovrin: Acad. B.V. Petrovsky Russian Surgery Research Center, Russian Academy of Medical Sciences; Research Institute of Nutrition, Russian Academy of Medical Sciences
T. N. Galyan: Acad. B.V. Petrovsky Russian Surgery Research Center, Russian Academy of Medical Sciences; Research Institute of Nutrition, Russian Academy of Medical Sciences
B. S. Kaganov: Acad. B.V. Petrovsky Russian Surgery Research Center, Russian Academy of Medical Sciences; Research Institute of Nutrition, Russian Academy of Medical Sciences
E. N. Kutyreva: Acad. B.V. Petrovsky Russian Surgery Research Center, Russian Academy of Medical Sciences; Research Institute of Nutrition, Russian Academy of Medical Sciences
A. I. Zubovich: Acad. B.V. Petrovsky Russian Surgery Research Center, Russian Academy of Medical Sciences; Research Institute of Nutrition, Russian Academy of Medical Sciences

DOI: https://doi.org/10.23873/2074-0506-2011-0-2-3-24-28
Journal volume & issue: Vol. 0, no. 2-3
pp. 24 – 28

Abstract

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The paper describes two clinical examples of successful related liver fragment transplantation for type 1 glycogenosis in a one-year-old boy and a 6-year-old girl. The given first successful clinical experience suggests that liver fragments for type 1 glycogenoses can be transplanted from live related donors and offers promise for the radical treatment of patients with this pathology.

Published in Трансплантология (Москва)

ISSN: 2074-0506 (Print); 2542-0909 (Online)
Publisher: N.V. Sklifosovsky Research Institute for Emergency Medicine of Moscow Healthcare Department
Country of publisher: Russian Federation
LCC subjects: Medicine
Website: http://www.jtransplantologiya.ru/jour

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Abstract

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