Мать и дитя в Кузбассе (Aug 2020)
CONGENITAL MALFORMATION OF THE LIVER IN A NEWBORN (CLINICAL CASE)
Abstract
Congenital hyperplasia of the intrahepatic bile ducts refers to early fetopathy. It represents a «bizarre» proliferation of bile ducts in the portal tract with excessive development of connective tissue. A frequent complication of this defect is the attachment of secondary purulent cholangitis. When combined with small cystic kidney disease, death occurs from renal failure in the first days of life.