Case Reports in Nephrology and Dialysis (May 2017)

Erdheim-Chester Disease Presenting with Secondary Hypertension as a Result of Bilateral, Proximal Renal Artery Stenosis: A Case Report

  • Farid Arman,
  • Hania Shakeri,
  • Niloofar Nobakht,
  • Anjay Rastogi,
  • Mohammad Kamgar

DOI
https://doi.org/10.1159/000471760
Journal volume & issue
Vol. 7, no. 2
pp. 55 – 62

Abstract

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Erdheim-Chester disease (ECD) is a rare, non-Langerhans cell histiocytosis presenting most commonly with bone and central nervous system symptoms, including but not limited to bone pain and diabetes insipidus. We present a known case of ECD, which was referred for secondary hypertension workup and diagnosed with severe, proximal, bilateral renal artery stenosis.

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