Surgical Treatment of Chest Deformity in a Patient with Poland Syndrome. Clinical Case Report

Abstract

Ablaikhan Kazbekov,1,2 Olzhas Bekarisov,1 Kairat Tazhin1 1National Scientific Center for Traumatology and Orthopedics Named After Academician N.D. Batpenov, Ministry of Health of the Republic of Kazakhstan, Astana, Kazakhstan; 2Astana Medical University, Astana, KazakhstanCorrespondence: Ablaikhan Kazbekov, Email [email protected]: Poland syndrome is a rare congenital syndrome that is characterized by partial or complete unilateral absence of the pectoralis major muscle, congenital malformation of the hand and deformation of the chest. Often the patients has abnormalities of the nipple-areolar complex. Here, we present a case of surgical treatment of local chest deformity with patient with Poland syndrome.Case Presentation: We observed a patient, an 18-year-old man. The parents noticed the deformation of the chest from birth. The patient did not receive any treatment until adulthood. The patient contacted our clinical research center to correct chest deformity. After clinical and diagnostic procedures, the patient underwent surgical operation: open thoracoplasty with installation of a wire-frame construction. The early postoperative period was uneventful. Early postoperative outcome was assessed 6 months after surgery.Conclusion: Our experience shows that thoracoplasty using a wire-frame construction is a good method for correcting local chest deformities in patients with Poland syndrome.Keywords: Poland syndrome, chest deformity, surgery, case report

Keywords

• poland syndrome
• chest deformity
• surgery
• case report