Cystic Medial Degeneration Leading to Aortic Aneurysm and Aortic Regurgitation

Abstract

Aortic aneurysm is a rare, but mostly fatal condition; the incidence is 5.9 new aneurysm/100,000 person-years with median age of 65 years for men and 77 years for women. It becomes still rarer when the cause is idiopathic and is associated with aortic regurgitation. Most of these patients present with aortic regurgitation and on investigation aneurysm is detected. Owing to its rarity and disguised presentation it is important to be aware of this entity. This case is being presented not only because of its rarity, but also because of its atypical presentation.

Keywords

• Atherosclerosis
• cystic medial degeneration
• Marfan′s syndrome