Indian Journal of Endocrinology and Metabolism (Jan 2013)
Sarcomatous transformation (Leiomyosarcoma) in polyostotic fibrous dysplagia
Abstract
Malignant changes in polyostotic fibrous dysplasia are very rare. Most common malignancies reported are osteosarcoma and fibrosarcoma, chondrosarcoma and malignant fibrous histiocytoma. Here, we report a previously diagnosed case of fibrous dysplasia who has developed leiomyosarcoma; diagnosis of which was delayed for about one year despite repeated fine needle aspiration and open biopsy.
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