Brazilian Journal of Cardiovascular Surgery (Jul 2023)

Reverse Potts for the Treatment of Severe Idiopathic Pulmonary Hypertension in Children

  • Marcelo Frederigue de Castro,
  • Edmundo Clarindo Oliveira,
  • Maria Carmo Pereira Nunes,
  • Carla de Oliveira,
  • Maria Gabriela Costa de Almeida,
  • Jose Augusto Almeida Barbosa

DOI
https://doi.org/10.21470/1678-9741-2022-0320
Journal volume & issue
Vol. 38, no. 4

Abstract

Read online Read online

ABSTRACT Idiopathic pulmonary arterial hypertension is a rare and progressive disease with poor prognosis. Many patients progressively worsen even when using combinations of specific drugs for its treatment. Herein, we present our experience in the management of three children with severe pulmonary arterial hypertension refractory to clinical treatment who underwent Potts surgery in addition to clinical treatment.

Keywords