The Rosai Dorfman Syndrome–The Report of A Rare Case

Abstract

Rosai Dorfman syndrome known as Sinus Histiocytosis with Massive Lymphadenopathy (SHML) is an uncommon benign systemic histio-proliferative disease which affects lymph nodes, most often those of the neck (cervical lymphadenopathy). The characteristic histological feature is lymphophagocytosis which is specific for this syndrome. Evidence based survey reveals that many cases that have been reported in india are from medical fraternity other than dental colleagues. As dental professionals we document a rare case of Rosai – Dorfman syndrome, reported to the department of oral and maxillofacial pathology with the cheif complaint of swelling in the neck region.

Keywords

• the rosai-dorfman disease
• histiocytosis
• cervical lymph nodes
• emperipolesis