Journal of Nepal Medical Association (Jan 2003)
SICKLE CELL DISEASE - CASE REPORTS
Abstract
ABSTRACT Sickle cell diseases are inherited hematological diseases, prevalent in certain parts of the world. We report two cases of sickle cell diseases, first being sickle cell b-thalassaemia and second homozygous sickle cell disease (SS). Our first case was 5 year old boy presenting with hemolytic anaemia & hepatosplenomegaly having sickle cell b-thalassaemia disease . Second case was 17 years female presenting with hemolytic anaemia & joint pain having homozygous sickle cell disease. Key Words: Homozygous sickle cell disease, sickle cell b - thalassaemia, hemoglobin electrophoresis.