Cancer Biology & Medicine (Sep 2015)

Acute coronary syndrome: a rare case of multiple endocrine neoplasia syndromes with pheochromocytoma and medullary thyroid carcinoma

  • Alessadro Maloberti,
  • Paolo Meani,
  • Roberto Pirola,
  • Marisa Varrenti,
  • Marco Boniardi,
  • Anna Maria De Biase,
  • Paola Vallerio,
  • Edgardo Bonacina,
  • Giuseppe Mancia,
  • Paola Loli,
  • Cristina Giannattasio

DOI
https://doi.org/10.7497/j.issn.2095-3941.2015.0016
Journal volume & issue
Vol. 12, no. 3
pp. 255 – 258

Abstract

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Pheochromocytoma is a tumor arising from neuroectodermal chromaffin tissues in the adrenal gland or extra-adrenal paraganglia (paragangliomas). The prevalence of the tumor is 0.1%-0.6% in the hypertensive population, of which 10%-20% are malignant. Pheochromocytoma produces, stores, and secretes catecholamines, as well as leads to hypertensive crisis, arrhythmia, angina, and acute myocardial infarction without coronary artery diseases. We report a case of acute coronary syndrome (ACS) with a final diagnosis of multiple endocrine neoplasia with pheochromocytoma and medullary thyroid carcinoma (MTC).

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