Recurrent pneumothorax in a young female with pulmonary lymphangiomyomatosis: A case report and overview of literature

Abstract

Lymphangiomyomatosis (LAM) is a rare cystic interstitial lung disease that exclusively affects women of child bearing age and is associated with vascular proliferation of smooth muscle cells in the lung. We report a case of young female with pulmonary LAM presenting with recurrent pneumothorax.

Keywords

• Cystic disease
• lymphangiomyomatosis
• pneumothorax
• pulmonary