Oral manifestations of lamellar ichthyosis: A rare case report

Abstract

The ichthyoses are a heterogeneous group of disorders with both inherited and acquired forms. Autosomal recessive congenital ichthyosis (ARCI) is a heterogeneous group of disorders that present at birth with the generalized involvement of skin without other systemic manifestations. Lamellar itchthyosis (LI) is a nonsyndromic itchthyosis, which comes under the umbrella of ARCI. Little is only known about the oral manifestations of this disorder. We report a case of LI with oral manifestations.

Keywords

• Autosomal recessive congenital ichthyosis
• lamellar itchthyosis
• nonsyndromic itchthyosis
• oral manifestations of itchthyosis