Oncology Reviews (Dec 2011)

Characteristics and management of pancreatic lesions in Von Hippel-Lindau disease: a systematic literature review

  • Giuseppe Lombardi,
  • F. Zustovich,
  • S. Zovato,
  • D. Fiore,
  • A. Cappetta,
  • D. Pastorelli

DOI
https://doi.org/10.4081/oncol.2009.103
Journal volume & issue
Vol. 3, no. 2

Abstract

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Von Hippel-Lindau disease is a rare autosomal dominant inherited disorder that predisposes the occurrence of cysts and various types of cancers such as hemangioblastoma, pheochromocytoma, renal cell carcinoma and more rarely pancreatic tumors. In this review, we analyze the characteristics and management of pancreatic lesions, in particular cysts and neuroendocrine tumors, in Von Hippel-Lindau disease.

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