Type I Segmental Darier’s Disease: Successful Treatment with Oral Acitretin- A Case Report

Abstract

Unilateral type I segmental Darier’s Disease (DD) is a rare variant of DD. It is characterised by eruptions which are erythematous and keratotic papules. The authors, hereby reporting a case of an 18-year-old male patient, who presented with waxy hyperpigmented keratotic papules on the right-side of the trunk and lower limb and was confirmed by histopathology and treated with oral acitretin, 25 mg once a day, which showed a marked clinical improvement within four months.

Keywords

• genodermatosis
• histopathology
• hyperpigmentation
• oral retinoids
• papules