Indian Journal of Ophthalmology (Jan 2014)
Cystoid macular edema in a patient with Danon disease
- Heather G Mack
Affiliations
- Heather G Mack
- DOI
- https://doi.org/10.4103/0301-4738.109524
- Journal volume & issue
-
Vol. 62,
no. 12
pp. 1161 – 1163
Abstract
To report a patient with Danon retinopathy with cystoid macular edema treated with topical dorzolamide 2% eye drops and oral acetazolamide. A 37-year-old Caucasian man with Danon disease treated with topical and oral carbonic anhydrase inhibitors participated in the study. Examinations performed before and during treatment included visual acuity (VA), spectral-domain optical coherence tomography, and electroretinography. Following total 48 weeks of treatment, VA decreased from 20/30 OD, 20/200 OS, to 20/40 OD, CF OS. The mean central retinal thickness was unchanged from baseline 263 μm OD , 226 μm OS, after treatment 283 μm OD and 202 μm OS. In our case, carbonic anydrase inhibitors were not effective. However, a general recommendation cannot be given based on a single case.
Keywords
- Malignant glaucoma
- pseudophakic
- surgical management
- zonulo-hyaloido-vitrectomy
- Automated retinal imaging
- diabetic retinopathy
- screening
- Low vision
- low vision aids
- quality of life
- Children
- congenital cataract
- hydrophobic acrylic intraocular lens
- intraocular lens implantation
- myopic shift
- polymethyl methacrylate
- Cost-effectiveness
- glaucoma
- pharmacoeconomics
- External limiting membrane
- macular hole
- predictors
- Optic nerve head drusen
- optical coherence tomography
- papilledema
- pseudopapilloedema
- Crowding
- logMAR chart
- refractive error
- screening
- visual acuity
- Acute retinal pigment epithelitis
- multifocal electroretinogram
- optical coherence tomography
- Anterior chamber
- intraocular parasite
- Linguatula serrata (tongue worm)
- subluxated lens
- vitrectomy
- Carbonic anhydrase inhibitor
- Danon disease
- ERG
- retinal disease
- SD-OCT
