Revisiting Rosai Dorfman disease: A rare histiocytic disorder with nodal and extranodal involvement

Abstract

Rosai Dorfman disease is a rare but benign and self-limiting disorder. A case of Rosai Dorfman disease in a 16-year-old female with classic radiological and pathological findings is presented. T2W hypointense signal of the soft tissue masses was a distinguishing MRI feature. Contribution: Rosai Dorfman disease is often overlooked in the differentials of lymphadenopathy and soft tissue masses on account of its rarity. This case report comprehensively discusses the imaging approach to this rare disorder.

Keywords

• rosai dorfman disease
• emperipolesis
• massive lymphadenopathy
• sinus histiocytosis
• histiocytosis.