Persistent pulmonary interstitial emphysema in a case of Langerhans cell histiocytosis

Abstract

We present the case of a 10-month-old boy with multisystem Langerhans cell histiocytosis showing thin-walled lung cysts along with computed tomography (CT) evidence of persistent pulmonary interstitial emphysema (PPIE), in the absence of pneumothorax or pneumomediastinum. Follow-up CT performed after 6 months demonstrated complete resolution of interstitial emphysema.

Keywords

• langerhans cell histiocytosis
• lung cysts
• persistent pulmonary interstitial emphysema