Generalized scleroderma in a girl

Abstract

Scleroderma is an autoimmune condition of unknown causes that can be presented affecting only the skin, called morphea, or affecting body systems. As part of the morphea the generalized form is not very common in childhood. This study presents the case of a girl who was taken to "Mártires de Las Tunas" Provincial Pediatric Hospital with generalized cutaneous manifestations, mainly in the trunk and limbs, not including the face, and characterized by sclerotic hyperpigmented and hypopigmented lesions which do not allow pinching the skin. Several investigations were performed ruling out systemic affectations and the diagnosis of generalized scleroderma was confirmed by means of a histopathologic study. Mother and patient were given advice and the topic and systemic treatment was adjusted according to the degree of the condition. The patient progressed satisfactorily.

Keywords

• scleroderma, systemic
• esclerodermia localizada
• sclerosis
• rheumatic diseases