Surgical Experiences and Results of the Management of Double Chambered Right Ventricle

Abstract

Objective: To identify anatomical features, association and surgical results of patient with double chambered right ventricle. Study Design: Prospective longitudinal study. Place and Duration of Study: The Children Hospital and Institute of Child Health, Lahore Pakistan, from Jan 2013 to Dec 2018. Methodology: All patients presenting with mid cavity right ventricular outflow tract obstruction were included. All patients’ demographic data, clinical profile, diagnostic reports, associated anomalies, and surgical data were recorded. Results: Fifty-two patients with mid-cavity right ventricular outflow tract obstruction of various ages (from 6 months to 31 years) were included. Ten patients (19%) presented in infancy. Forty-six patients (89%) had an associated ventricular septal defect, ten (15%) had aortic valve right coronary cusp prolapse with varying degrees of aortic regurgitation. All patients had a right ventricular mid-cavity and infundibular muscle resection via the tricuspid valve. There was one hospital death due to an intraoperative global neurologic catastrophe. The median follow-up after surgery was 37.5 months. There was no late death. Conclusion: Doubly committed Ventricular septal defect with aortic valve right coronary cusp prolapse with varying degree of aortic regurgitation and absence of subaortic stenosis is a new finding in our study. Early and Medium-term surgical results of repair are excellent.

Keywords

• Aortic Insufficiency, Double Chambered Right Ventricle, Mid Cavity Right Ventricular Outflow Tract Obstruction, Right Coronary Cusp Prolapse