Hearing loss induced by primary antiphospholipid syndrome, and its improvement by cochlear implant: A clinical case report

Abstract

AbstractOne of the less common clinical manifestations of antiphospholipid syndrome (APS) is hearing loss, so early diagnosis and the use of a cochlear implant may be a viable alternative. Patient with hearing loss and anacusis, associated with positive aPL and APS, who underwent a cochlear implant (Rondo 2, Med-El) to correct hearing that is evaluated with impedance telemetry, with adequate responses were found in the 12 pairs of electrodes, a neuronal response telemetry with electrically evoked compound action potential (eCAP) and normal right hearing was achieved by audiogram (maximum phonemic discrimination threshold of 20% at 110 dB initial and 90% at 70 dB final). APS is a rare pathology which requires a high sense of alert on the health team to avoid delays in the diagnosis and treatment of hearing loss, and to establish the cochlear implant as a viable and useful alternative in the hearing recovery by APS.

Keywords

• Pediatric antiphospholipid syndrome
• cochlear implantation
• hearing loss
• audiometry
• pediatric