Journal of Cardiothoracic Surgery (Aug 2017)

Doege-potter syndrome: a report of a histologically benign but clinically malignant case

  • Do Wan Kim,
  • Kook Joo Na,
  • Ju Sik Yun,
  • Sang Yun Song

DOI
https://doi.org/10.1186/s13019-017-0630-4
Journal volume & issue
Vol. 12, no. 1
pp. 1 – 4

Abstract

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Abstract Background Solitary fibrous tumors of the pleura (SFTPs) are relatively rare tumors that originate from mesenchymal cells of submesothelial tissue of the pleura. Most patients with SFTPs are asymptomatic; however, pleuritic chest pain, cough, and dyspnea can develop. If hypoglycemia is associated with a solitary fibrous tumor, it is referred to as the Doege-Potter syndrome. Case presentation A 70-year-old man had visited our hospital with a chief complaint of dyspnea, and he was diagnosed as having a solitary fibrous tumor. A few years later, he developed hypoglycemia, and he underwent excision of the mass. Conclusion Occasionally, SFTPs induce several paraneoplastic events, such as hypertrophic osteoarthropathy. We described here a patient with an SFTP with Doege-Potter syndrome who was successfully treated with complete resection. Although lesions can be histologically benign, they can clinically present with malignant features.

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