Percutaneous sequential closure of an Abernethy malformation: A case report

Asad Malik, MD; Muhammed Ebrahim Patel, MD; Daniel Ganger, MD; Elias Hohlastos, MD; Ahsun Riaz, MD

Radiology Case Reports (Sep 2023)

Percutaneous sequential closure of an Abernethy malformation: A case report

Asad Malik, MD,
Muhammed Ebrahim Patel, MD,
Daniel Ganger, MD,
Elias Hohlastos, MD,
Ahsun Riaz, MD

Affiliations

Asad Malik, MD: Division of Interventional Radiology, Department of Radiology, Northwestern University, 676 N. St. Clair, Suite 800, Chicago, IL, USA
Muhammed Ebrahim Patel, MD: Division of Interventional Radiology, Department of Radiology, Northwestern University, 676 N. St. Clair, Suite 800, Chicago, IL, USA
Daniel Ganger, MD: Department of Medicine, Section of Gastroenterology/Hepatology, Northwestern University, Chicago, IL, USA
Elias Hohlastos, MD: Division of Interventional Radiology, Department of Radiology, Northwestern University, 676 N. St. Clair, Suite 800, Chicago, IL, USA
Ahsun Riaz, MD: Division of Interventional Radiology, Department of Radiology, Northwestern University, 676 N. St. Clair, Suite 800, Chicago, IL, USA; Corresponding author.

Journal volume & issue: Vol. 18, no. 9
pp. 3135 – 3139

Abstract

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Abernethy malformation (congenital extrahepatic portosystemic shunt [CEPS]) is rare and is characterized by an aberrant connection between the portal and systemic veins, bypassing the liver. It can have varying presentations and can lead to severe complications if left untreated. It is usually diagnosed incidentally on abdominal imaging. Occlusion venography and measurement of portal pressures (pre- and postocclusion) is an important step in management. Complete occlusion of the malformation in cases where the portal veins in the liver are very small and the gradient is more than 10 mm Hg, can potentially lead to acute portal hypertensive complications, such as porto-mesenteric thrombosis. We report a case of Abernethy malformation diagnosed on an abdominal computed tomography scan that presented with neurological symptoms and was successfully managed by interventional radiology via endovascular closure through placement and sequential occlusion of 2 metal stents.

Published in Radiology Case Reports

ISSN: 1930-0433 (Online)
Publisher: Elsevier
Country of publisher: United States
LCC subjects: Medicine: Medicine (General): Medical physics. Medical radiology. Nuclear medicine
Website: http://www.journals.elsevier.com/radiology-case-reports/

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