European Journal of Case Reports in Internal Medicine (Jan 2022)

Unicentric Castleman Disease and Pheochromocytoma

  • Rosana Maia,
  • Joana Couto,
  • José Diogo Martins,
  • Edgar Torre,
  • Diana Guerra

DOI
https://doi.org/10.12890/2022_003068

Abstract

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Castleman disease is an uncommon and heterogenous lymphoproliferative disorder which is classified as unicentric or multicentric depending on the number of lymph nodes involved. Each type has a different clinical presentation, aetiology, treatment and prognosis. We report the case of a young woman who presented with cervical lymphadenopathy and a retroperitoneal mass, and was diagnosed with unicentric Castleman disease and pheochromocytoma. We describe the diagnostic steps, the complications that developed, and the importance of the differential diagnosis in the evaluation of these patients.

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