Revista de Ciencias Médicas de Pinar del Río (Jun 2018)

Ewing's sarcoma of retroperitoneal presentation

  • Carlos Pérez Díaz

Journal volume & issue
Vol. 22, no. 5
pp. 973 – 980

Abstract

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Introduction: within the tumors of small, round, blue cells are a heterogeneous range of neoplasm in which immunohistochemical or other special techniques are imperative to be able to differentiate, or in many cases, only by exclusion approaching the possible histogenesis of the tumor in any case, these tumors are all highly undifferentiated, aggressive and almost always of a gloomy or very poor prognosis. Case Report: a 44-year-old male patient, with pathological history of acute lymphoblastic leukemia, with a complete remission of 10 year-evolution, who was assessed by presenting pain in the left lumbar region. A case study was performed and ultrasound revealed the presence of a retroperitoneal tumor. Surgery was decided on by exploratory laparotomy, and surgical excision of the tumor was performed. The patient recovery was satisfactory from the surgical procedure, however, the tumor recurred in a period of 1 month and the treatment with radiotherapy and cytostatics started with an unfavorable prognosis. Conclusions: the definitive diagnosis was performed by immunohistochemical study, resulting in a peripheral neuroectodermal tumor. The definitive diagnosis is made by the immunohistochemical study, the result being a peripheral neuroectodermal tumor or Ewing's sarcoma. Given that it is a rare diagnosis in adults after the second decade of life and often confused with other tumors, such as melanomas or carcinomas, the case is reported.

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