Papillon-Lefevre Syndrome - A Case Report

Abstract

Papillon-Lefevre Syndrome is a rare autosomal recessive disorder of Palmoplantar Keratinisation (PPK) in which there is a unique association of the palmoplantar hyperkeratosis and premature loss of both deciduous and permanent teeth. In most cases, the PPK is noted within the first 3 years of life. Usually the patient becomes edentulous by 20 years of age. A case of 13 years old female with AS sydrome is discussed in this article.

Keywords

• Syndrome
• Palmoplantar
• Keratosis
• Aggressive Periodontitis.