POS-432 DELETION OF THE POLYCYSTIN-1 COILED-COIL MOTIF LEADS TO A SEVERE FUNCTIONAL HYPOMORPHIC ADPKD ALLELE IN MICE: INSIGHTS INTO INTRACELLULAR MECHANISMS
M.L. PAUL,
A. Kurbegovic,
M. Trudel
Affiliations
M.L. PAUL
Institut de Recherches Cliniques de Montréal, Molecular Genetic and Development, Montreal, Canada
A. Kurbegovic
Institut de Recherches Cliniques de Montréal, Molecular Genetic and Development, Montreal, Canada
M. Trudel
Institut de Recherches Cliniques de Montréal, Molecular Genetic and Development, Montreal, Canada